Factor I Deficiency

Factor I Deficiency

Factor I deficiency is a collective word for three rare inherited bleeding disorder that is caused by complications with factor I when the clotting reaction is blocked too soon causing the blood clot to not form. The deficiency of the clotting factor is either the body does not make enough fibrinogen or the fibrinogen is not working like it should.

According to hemophilia.org, fibrinogen deficiencies can be quantitative or qualitative, depending on whether the fibrinogen is deficient or defective.

The quantitative disorders are afibrinogenemia,when fibrinogen is absent, and hypofibrinogenemia, when some protein with normal structure  is present but below levels needed for normal clotting.

Dysfibrinogenemia is a qualitative disorder in which normal amounts of fibrinogen are manufactured by the liver, but they don’t clot properly.

Factor I Deficiency Treatment

RiaSTAP is indicated for the treatment of acute bleeding episodes in patients with congenital fibrinogen deficiency (CFD), including afibrinogenemia and hypofibrinogenemia.

HF Healthcare provides RiaSTAP used to treat factor 1 deficiency and can create a manageable care plan that works in concert with your physician and insurance payer. We are here to guide you to a healthy future!